The Most Important Rules of Prosthetic Care in PatientsSuffering from Hereditary Motorand Sensory Neuropathy(HMSN)
ZÁSADY PROTETICKÉ PÉČE U PACIENTŮS HEREDITÁRNÍ MOTORICKO-SENZORICKOUNEUROPATIÍ (HMSN)
V České republice žije asi 4000 pacientů postižených některým druhem dědičné neuropatie.Onemocnění se projevuje oslabením a svalovými atrofiemi s převahou distálně na dolních, pozdějii horních končetinách, a typickou defomitou nohy typu „pes excavatus – transversoplanus“. Tatoortopedická deformita je pro pacienta častým zdrojem bolestí, nestability, poruch při stoji a chůzia omezuje ho v běžných denních činnostech. Popsané obtíže lze do značné míry pozitivně ovlivnitsprávnou protetickou péčí, která by měla být součástí komplexní rehabilitace u všech pacientůs HMSN.Článek shrnuje zkušenosti s protetickou péčí u pacientů s HMSN, které jsme získali běhempětiletého fungovánímultidisciplinárního centra pro pacienty s hereditárnímineuropatiemi ve Fakultnínemocnici v Motole.
Klíčová slova:
hereditární motoricko-senzorická neuropatie, choroba Charcot-Marie-Tooth,deformita nohy, protetika, ortopedické vložky do bot, AFO ortéza
Authors:
A. Kobesová 1; P. Smetana 2; J. Suzan 1; V. Smetana 2; L. Baránková 3; O. Horáček 1
Authors‘ workplace:
Klinika rehabilitace FN Motol, Praha 2Ortopedická klinika dětí a dospělých FN Motol, Praha3Klinika dospělé neurologie FN Motol, Praha
1
Published in:
Rehabil. fyz. Lék., , 2004, No. 4, pp. 169-175.
Category:
Overview
There are approximately 4000 patients suffering from some form of hereditary neuropathy in theCzech Republic. The most typical clinical symptoms are muscular weakness and atrophy affectingprimarily the distal parts of the lower and ultimately the upper extremities and characteristic footdeformity: high arch foot type with hammer toes and sagging transverse arch. Such foot deformityresults in pain and poor stability when standing and walking and limits the patient in many activitiesof everyday. It is possible to alleviate the consequences of feet deformity by correct prosthetic carewhich should be an important part of complex rehabilitation in all patients suffering from HMSN. Inthis article we present our experience with prosthetic care during the 5 year existence of themulti-specialist center for patients suffering from HMSN in the University Hospital Motol, Prague,Czech Republic.
Key words:
hereditary motor and sensory neuropathy, Charcot-Marie-Tooth disease, footdeformity, prosthetic care, orthopedic insoles, ankle-foot orthosis
Labels
Physiotherapist, university degree Rehabilitation Sports medicineArticle was published in
Rehabilitation and Physical Medicine
2004 Issue 4
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